19 Biliary Disorders

Biliary Atresia

• closed/absent bile duct

Primary Biliary Cirrhosis

• without obstruction/mass/stones

• obstruction inside liver

• no jaundice/RUQ pain

• itching and very high alk phos

• can't get lipids out in bile

• RUQ US: nl bile duct

• ultimately cirrhosis

Primary Sclerosing Cholangitis

• biliary tree stuck together. Bile can't flow

• primary biliary cirrhosis only intra ducts

• complication of ulcerative colitis

• scar, fibers form as result of inflammation, then strictures form

Diagnosis

• fibrous tissues laid down in circles around ducts

• beads on a string

Treatment

• cholangiocarcinoma risk

Cholangiocarcinoma